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<article article-type="abstract" dtd-version="1.0" xml:lang="en" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:mml="http://www.w3.org/1998/Math/MathML">
<front>
<journal-meta>
<journal-id journal-id-type="publisher-id">CC</journal-id>
<journal-id journal-id-type="nlm-ta">Cardiol Croat</journal-id>
<journal-title-group>
<journal-title>Cardiologia Croatica</journal-title>
<abbrev-journal-title abbrev-type="pubmed">Cardiol. Croat.</abbrev-journal-title>
</journal-title-group>
<issn pub-type="ppub">1848-543X</issn>
<issn pub-type="epub">1848-5448</issn>
<publisher><publisher-name>Croatian Cardiac Society</publisher-name></publisher>
</journal-meta>
<article-meta>
<article-id pub-id-type="publisher-id">CC 2023 18_9-10_259</article-id>
<article-id pub-id-type="doi">10.15836/ccar2023.259</article-id>
<article-categories><subj-group subj-group-type="heading"><subject>Extended Abstract</subject></subj-group>
<subj-group subj-group-type="subheading"><subject>Arrhythmias in valvular heart disease</subject></subj-group>
</article-categories>
<title-group>
<article-title>Mitral valve prolapse and sudden cardiac death</article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-0754-7194</contrib-id><name><surname>Zadro Kordi&#x0107;</surname><given-names>Ines</given-names></name><xref ref-type="aff" rid="aff1"><sup>1</sup></xref><xref ref-type="corresp" rid="cor1">*</xref></contrib>
<contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-0084-3465</contrib-id><name><surname>Peki&#x0107;</surname><given-names>Petar</given-names></name><xref ref-type="aff" rid="aff1"><sup>1</sup></xref></contrib>
<contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-1285-8042</contrib-id><name><surname>&#x010C;an&#x010D;arevi&#x0107;</surname><given-names>Ognjen</given-names></name><xref ref-type="aff" rid="aff1"><sup>1</sup></xref></contrib>
<contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-3189-8661</contrib-id><name><surname>Fri&#x0161;&#x010D;i&#x0107;</surname><given-names>Tea</given-names></name><xref ref-type="aff" rid="aff1"><sup>1</sup></xref></contrib>
<contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0001-8664-3338</contrib-id><name><surname>Planini&#x0107;</surname><given-names>Zrinka</given-names></name><xref ref-type="aff" rid="aff1"><sup>1</sup></xref></contrib>
<contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-3177-3797</contrib-id><name><surname>&#x010C;erkez Habek</surname><given-names>Jasna</given-names></name><xref ref-type="aff" rid="aff1"><sup>1</sup></xref></contrib>
<contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-9707-6946</contrib-id><name><surname>Kordi&#x0107;</surname><given-names>Kre&#x0161;imir</given-names></name><xref ref-type="aff" rid="aff2"><sup>2</sup></xref></contrib>
<contrib contrib-type="author"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-4488-0559</contrib-id><name><surname>&#x0160;iki&#x0107;</surname><given-names>Jozica</given-names></name><xref ref-type="aff" rid="aff1"><sup>1</sup></xref></contrib>
<aff id="aff1"><label>1</label><institution>University Hospital &#x201C;Sveti Duh&#x201D;</institution>, <addr-line>Zagreb</addr-line>, <country country="hr">Croatia</country></aff>
<aff id="aff2"><label>2</label><institution>University Hospital Centre &#x201C;Sestre milosrdnice&#x201D;</institution>, <addr-line>Zagreb</addr-line>, <country country="hr">Croatia</country></aff>
</contrib-group>
<author-notes>
<corresp id="cor1"><label>*</label>ADDRESS FOR CORRESPONDENCE: Ines Zadro Kordi&#x0107;, Klini&#x010D;ka bolnica Sveti Duh, Sveti Duh 64, HR-10000 Zagreb, Croatia. / Phone: +385-91-7940-161 / E-mail: <email xlink:href="ineszadro@gmail.com">ineszadro@gmail.com</email></corresp></author-notes>
<pub-date pub-type="epub-ppub"><month>08</month><year>2023</year></pub-date>
<volume>18</volume>
<issue>9-10</issue>
<fpage>259</fpage>
<lpage>259</lpage>
<history>
<date date-type="received"><day>28</day><month>07</month><year>2023</year></date>
<date date-type="accepted"><day>13</day><month>08</month><year>2023</year></date>
</history>
<permissions>
<copyright-statement>Croatian Cardiac Society</copyright-statement>
<copyright-year>2023</copyright-year>
<copyright-holder>Croatian Cardiac Society</copyright-holder>
</permissions>
<kwd-group kwd-group-type="author"><title>KEYWORDS: </title><kwd>mitral valve prolapse</kwd><kwd>mitral regurgitation</kwd><kwd>sudden cardiac death</kwd><kwd>implantable cardioverter defibrillator</kwd></kwd-group>
</article-meta>
</front>
<body>
<p><bold>Introduction</bold>: Mitral valve prolapse (MVP) is a common condition that affects up to 3% of the population. It is usually benign, but a small subset of patient has an increased risk of malignant ventricular arrhythmias and sudden cardiac death. (<xref ref-type="bibr" rid="r1"><italic>1</italic></xref>, <xref ref-type="bibr" rid="r2"><italic>2</italic></xref>)</p>
<p><bold>Case report</bold>: We present a previously healthy 56 years old female patient with history of palpitations. In May 2023, she was hospitalized after out-of-hospital cardiac arrest with ventricular fibrillation (VF) as the initial rhythm. After successful resuscitation, she regained full consciousness. Serum electrolytes were within normal range at admission. Electrocardiogram was uneventful. Echocardiography revealed normally sized left ventricle with preserved ejection fraction and severe mitral regurgitation due to posterior leaflet prolapse (P2 scallop) (<xref ref-type="fig" rid="f1"><bold>Figure 1</bold></xref>). No mitral annular disjunction (MAD) was visualized. No heart rhythm disturbances were registered during monitoring. Coronary angiography found no stenosis of coronary arteries. Implantable cardioverter defibrillator (ICD) was implanted for secondary prevention of sudden cardiac death. She was discharged with metoprolol and amiodarone. On follow up visit no heart rhythm disturbances were noticed on ICD interrogation. The patient is scheduled for cardiac surgery (mitral valve repair or replacement).</p>
<fig id="f1" position="float" fig-type="figure"><label>FIGURE 1</label><caption><p>Three-dimensional transthoracic and transesophageal echocardiography showing mitral valve prolapse (P2 scallop).</p></caption><graphic xlink:href="CC202318_9-10_259-f1"></graphic></fig>
<p><bold>Conclusion</bold>: Mitral valve prolapse is becoming increasingly recognized as an important phenomenon which can lead to malignant ventricular arrhythmias and sudden cardiac death. We presented a patient who survived sudden cardiac arrest. No predisposing conditions were found other than mitral valve prolapse. The patient is scheduled for cardiac surgery following the implantation of an ICD.</p>
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<ref-list>
<title>LITERATURE</title>
<ref id="r1"><label>1</label><mixed-citation publication-type="journal"><person-group person-group-type="author"><name><surname>Sabbag</surname><given-names>A</given-names></name><name><surname>Essayagh</surname><given-names>B</given-names></name><name><surname>Barrera</surname><given-names>JDR</given-names></name><name><surname>Basso</surname><given-names>C</given-names></name><name><surname>Berni</surname><given-names>A</given-names></name><name><surname>Cosyns</surname><given-names>B</given-names></name><etal/></person-group> <article-title>EHRA expert consensus statement on arrhythmic mitral valve prolapse and mitral annular disjunction complex in collaboration with the ESC Council on valvular heart disease and the European Association of Cardiovascular Imaging endorsed cby the Heart Rhythm Society, by the Asia Pacific Heart Rhythm Society, and by the Latin American Heart Rhythm Society.</article-title> <source>Europace</source>. <year>2022</year> December 9;<volume>24</volume>(<issue>12</issue>):<fpage>1981</fpage>&#x2013;<lpage>2003</lpage>. <pub-id pub-id-type="doi">10.1093/europace/euac125</pub-id><pub-id pub-id-type="pmid">35951656</pub-id></mixed-citation></ref>
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</ref-list>
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</article>
